Unveiling the Heart: A Rare Case of Double-Chambered Left Ventricle in a Patient with Coronary Artery Disease (QF_TH_055)

Thursday, January 30, 2025

4:20 PM – 4:30 PM East Coast USA Time

Location: Blue Room PreFunction

Presenting Author(s)

VS

Vinícius Cardoso Serra, MD

Fellow in Cardiovascular Computed Tomography and Magnetic Resonance
Instituto do Coração do Hospital das Clínicas da Faculdade de Medicina da Universidade de São Paulo, Brazil

Primary Author(s)

VS

Vinícius Cardoso Serra, MD

Fellow in Cardiovascular Computed Tomography and Magnetic Resonance
Instituto do Coração do Hospital das Clínicas da Faculdade de Medicina da Universidade de São Paulo, Brazil

Co-Author(s)

AV

André Vaz, MD

Radiologist
Incor, Brazil
AQ

Antonio Carlos F. Queiroz Filho, MD

Fellow in cardiovascular imaging
Instituto do Coração, Brazil
MB

Marina Souto da Cunha Brendel Braga, MD

Fellowship in cardiovascular imaging
InCor - Instituto do coração HCFMUSP, Brazil
ID

Ingrid Debaco, MD

Fellowship
Instituto do Coração da Faculdade de Medicina da Universidade de São Paulo ( InCor - FMUSP), Brazil
WI

Walther Y. Ishikawa, MD

assistant doctor
InCor - Instituto do Coração do Hospital das Clínicas da FMUSP, Brazil

Description of Clinical Presentation:

A 61-year-old male presented with chest pain and fatigue during minimal exertion. His medical history includes dyslipidemia and significant three-vessel coronary artery disease, identified during a coronary angiogram in 2017. Recently, his symptoms have worsened, leading to further evaluation through cardiac imaging.

Diagnostic Techniques and Their Most Important Findings:

Cardiac MRI revealed a double-chambered left ventricle (DCLV), a rare congenital anomaly where a prominent muscular septum divides the left ventricular cavity (Figure 1). The accessory chamber measured 61x32 mm and communicated with the main chamber (Figure 2). The MRI showed preserved global left ventricular systolic function, with an ejection fraction of 62%. Late gadolinium enhancement showed no evidence of myocardial fibrosis (Figure 3).

Learning Points from this Case:

This case highlights the value of cardiac MRI in detecting rare congenital heart abnormalities like double-chambered left ventricle (DCLV) in adults. The combination of DCLV with coronary artery disease adds complexity to the patient’s management. The absence of fibrosis offers a positive outlook, as timely treatment may prevent further progression. Regular follow-up with advanced imaging will be essential for monitoring the condition and guiding future interventions.